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The nevus followed the lines of Blaschko. On examination, she had a flat, soft, velvety, hyperpigmented linear nevus along the entire right arm, extending to the neck and then downward parallel to the mid-spinal line. There was no history of epilepsy, mental retardation or consanguinity. There was no family history of a similar disorder. Ī girl aged 3 years and 8 months presented with enlargement of both feet with macrodactyly, swelling on the left side of the flank, a hyperpigmented nevus and multiple soft subcutaneous swellings over the chest and abdomen. We present a patient with this exceedingly rare disorder, estimated to affect 100-200 individuals worldwide and having a prevalence less than 1 per 1,000,000 live births. Partial gigantism of a limb or digital overgrowth is pathognomonic with an unusual body habitus and often, cerebriform thickening of soles of feet. The disease was named after the Greek god Proteus in order to stress the polymorphic nature of the clinical presentation. Major clinical findings include hemihypertrophy, symmetric megalodactyly, sub-cutaneous masses (vascular, lymphatic and lipomatous), epidermal nevi and skull hyperostosis. It is a rare condition that can be loosely categorized as a hamartomatous disorder with great clinical variability. #Download proteus 87 64 BitThis would be compatible with both 32 bit and 64 bit windows.Proteus syndrome was first identified by Michel Cohen in 1979 and named by Rudolf Wiedmann in 1983. This is complete offline installer and standalone setup for Proteus Professional 8.7 SP3. Proteus Professional 8.7 SP3 Free DownloadĬlick on below button to start Proteus Professional 8.7 SP3 Free Download.
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